| CASE REPORT |
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| Year : 2014 | Volume
: 9
| Issue : 2 | Page : 188-191 |
Pituitary stalk interruption syndrome: Case report of three cases with review of literature
Manish Gutch1, Sukriti Kumar2, Syed Mohd Razi1, Sanjay Saran1, Keshav Kumar Gupta1
1 Department of Endocrinology, LLRM Medical College, Meerut, India
2 Department of Radiodiagnosis, SGPGI, Lucknow, Uttar Pradesh, India
Correspondence Address:
Manish Gutch
D-15, LLRM Medical College, Meerut - 250 004, Uttar Pradesh
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/1817-1745.139363
Pickardt syndrome (Pickardt-Fahlbusch syndrome) is a rare congenital syndrome characterized by tertiary hypothyroidism caused by the interruption of the portal veins between hypothalamus and adenohypophysis. Typical features of this syndrome are tertiary hypothyroidism with low thyroid stimulating hormone, hyperprolactinemia and other pituitary hormone deficiencies. Pituitary stalk interruption syndrome is characterized by a triad of thin or interrupted pituitary stalk, aplasia or hypoplasia of the anterior pituitary and absent or ectopic posterior pituitary (EPP) seen on magnetic resonance imaging (MRI). It is a congenital anomaly of pituitary whose exact prevalence is unknown. In some cases, it is restricted to EPP or pituitary stalk interruption. We are presenting the case history along with MRI finding of three children's who presented with short stature and delayed puberty.
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