CASE REPORT |
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Year : 2016 | Volume
: 11
| Issue : 3 | Page : 252-254 |
Dyke–Davidoff–Masson syndrome: A rare cause of cerebral hemiatrophy in children
Pareshkumar A Thakkar, Reema Haresh Dave
Department of Pediatrics, Baroda Medical College, Vadodara, Gujarat, India
Correspondence Address:
Pareshkumar A Thakkar Baroda Medical College, Vadodara, Gujarat India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/1817-1745.193365
Dyke–Davidoff–Masson syndrome (DDMS) is an uncommon condition, in which the diagnosis is mainly done by various clinical presentations along with positive radiological findings. Patients have facial asymmetry, seizures, learning difficulties, and contralateral hemiparesis. The radiological discoveries of the same incorporate cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. Here, we report a case of a 10-year-old female child who presented with a single episode of convulsion, mental retardation, and contralateral hemiparesis. Magnetic resonance imaging of the brain showed unilateral atrophy of the left cerebral hemisphere with dilatation of ipsilateral lateral ventricle and ipsilateral sulcal prominence. These findings were suggestive of the diagnosis of DDMS.
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