| CASE REPORT |
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| Year : 2017 | Volume
: 12
| Issue : 3 | Page : 294-297 |
Endolymphatic sac tumor in von Hippel–Lindau disease: A rare case report
Rituparna Biswas1, Kalpana Kumari2, Subhash Gupta1, KP Haresh1, Anirban Halder3, GK Rath1
1 Department of Radiation Oncology, Dr. BRA IRCH, All India Institute of Medical Sciences, New Delhi, India
2 Department of Pathology, All India Institute of Medical Sciences, New Delhi, India
3 Department of Radiation Oncology, VMMC and Safdarjung Hospital, New Delhi, India
Correspondence Address:
K P Haresh
Department of Radiation Oncology, Dr. BRA IRCH, All India Institute of Medical Sciences, New Delhi
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/jpn.JPN_28_17
Endolymphatic sac tumor (ELST) is a rare papillary neoplasm with locally destructive behavior which can occur sporadically or in association with Von Hippel–Lindau (VHL) disease. We herein present a case of ELST associated with VHL disease in a 14-year-old girl and discuss clinico-radiological, immunohistopathologic findings, and management by staged surgery and postoperative radiotherapy to the residual lesion.
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