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Year : 2020  |  Volume : 15  |  Issue : 2  |  Page : 160-161

Amniotic band syndrome with placenta–encephalocele adhesion: An uncommon case

Division of Pediatric Neurosurgery, Santa Mônica Maternity School (SMMS), Maceió, Brazil

Date of Submission04-Dec-2019
Date of Decision29-Jan-2020
Date of Acceptance11-Feb-2020
Date of Web Publication30-Jun-2020

Correspondence Address:
Dr. Aldo Jose Ferreira da Silva
Division of Pediatric Neurosurgery, Santa Mônica Maternity School (SMMS), Maceió, Alagoas.
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Source of Support: None, Conflict of Interest: None

DOI: 10.4103/jpn.JPN_163_19

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Amniotic band syndrome is a rare condition that is associated with various malformations. Its etiology is controversial. The neuroimage shown here is of a newborn with placenta–encephalocele adhesion and other malformations that suggest amniotic band syndrome.

Keywords: Amniotic band syndrome, encephalocele, placenta, syndactyly

How to cite this article:
da Silva AJ. Amniotic band syndrome with placenta–encephalocele adhesion: An uncommon case. J Pediatr Neurosci 2020;15:160-1

How to cite this URL:
da Silva AJ. Amniotic band syndrome with placenta–encephalocele adhesion: An uncommon case. J Pediatr Neurosci [serial online] 2020 [cited 2023 Jun 6];15:160-1. Available from: https://www.pediatricneurosciences.com/text.asp?2020/15/2/160/288308

   Case Top

A newborn male infant, born to a 32-year-old primiparous mother via cesarean delivery at term, with an Apgar score of 7–8 points, presented with frontal placenta–encephalocele adhesion [Figure 1] and other malformations including cleft palate, syndactyly, and partial agenesis of the fingers of the right hand [Figure 1]. The finding from the karyotype examination was normal, with 46, XY chromosomal constitution. The patient died on the second day of life.
Figure 1: Right hand: syndactyly and partial agenesis of the fingers (dotted black arrow). Placenta–encephalocele adhesion (black arrow)

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Amniotic band syndrome or sequence is rare, with its incidence ranging from 1:1,200 to 1:15,000 live births. It appears as a collection of congenital malformations, from small constriction rings to major anomalies that compromise the vital organs.[1],[2] Its etiology is unknown, but two theories have been proposed to explain its pathogenesis: the Streeter’s intrinsic theory, according to which a defective local embryonic development explains the anomalies, and the Torpin’s extrinsic theory, in which a rupture of the amnion explains the anomalies.[3] When placentocranial adhesions occur, causative factors could include a short umbilical cord, an encephalocele, or intrauterine trauma.[4]

Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

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Conflicts of interest

There are no conflicts of interest.

   References Top

Sentilhes L, Verspyck E, Patrier S, Eurin D, Lechevallier J, Marpeau L. Amniotic band syndrome: pathogenesis, prenatal diagnosis and neonatal management. J Gynecol Obstet Biol Reprod 2003;32:693-704.  Back to cited text no. 1
Da Silva G, Cammarata-Scalisi F, González-Coria M, La Cruz MA, Rendon B. Síndrome de bridas amnióticas a propósito de 3 casos clínicos. [Amniotic band syndrome in 3 clinical cases.] Rev Chil Pediatr 2008;79:172-80. Portuguese.  Back to cited text no. 2
Nogueira FCS, Cruz RB, Machado LP, Ramos BLF, Madureira-Júnior JL, Pinto RZA. Síndrome da banda amniótica: relato de caso. [Amniotic band syndrome: A case report.] Rev Bras Ortop [Internet] 2011;46:56-62. Portuguese.  Back to cited text no. 3
Menekse G, Mert MK, Olmaz B, Celik T, Celik US, Okten AI. Placento-cranial adhesions in amniotic band syndrome and the role of surgery in their management: An unusual case presentation and systematic literature review. Pediatr Neurosurg 2015;50:204-9.  Back to cited text no. 4


  [Figure 1]

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1 Clinical assessment of the results of one-stage circular incision techniques for limb ring constriction due to amniotic band syndrome
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[Pubmed] | [DOI]


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