|Year : 2020 | Volume
| Issue : 2 | Page : 160-161
Amniotic band syndrome with placenta–encephalocele adhesion: An uncommon case
Aldo Jose Ferreira da Silva
Division of Pediatric Neurosurgery, Santa Mônica Maternity School (SMMS), Maceió, Brazil
|Date of Submission||04-Dec-2019|
|Date of Decision||29-Jan-2020|
|Date of Acceptance||11-Feb-2020|
|Date of Web Publication||30-Jun-2020|
Dr. Aldo Jose Ferreira da Silva
Division of Pediatric Neurosurgery, Santa Mônica Maternity School (SMMS), Maceió, Alagoas.
Source of Support: None, Conflict of Interest: None
| Abstract|| |
Amniotic band syndrome is a rare condition that is associated with various malformations. Its etiology is controversial. The neuroimage shown here is of a newborn with placenta–encephalocele adhesion and other malformations that suggest amniotic band syndrome.
Keywords: Amniotic band syndrome, encephalocele, placenta, syndactyly
|How to cite this article:|
da Silva AJ. Amniotic band syndrome with placenta–encephalocele adhesion: An uncommon case. J Pediatr Neurosci 2020;15:160-1
| Case|| |
A newborn male infant, born to a 32-year-old primiparous mother via cesarean delivery at term, with an Apgar score of 7–8 points, presented with frontal placenta–encephalocele adhesion [Figure 1] and other malformations including cleft palate, syndactyly, and partial agenesis of the fingers of the right hand [Figure 1]. The finding from the karyotype examination was normal, with 46, XY chromosomal constitution. The patient died on the second day of life.
|Figure 1: Right hand: syndactyly and partial agenesis of the fingers (dotted black arrow). Placenta–encephalocele adhesion (black arrow)|
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Amniotic band syndrome or sequence is rare, with its incidence ranging from 1:1,200 to 1:15,000 live births. It appears as a collection of congenital malformations, from small constriction rings to major anomalies that compromise the vital organs., Its etiology is unknown, but two theories have been proposed to explain its pathogenesis: the Streeter’s intrinsic theory, according to which a defective local embryonic development explains the anomalies, and the Torpin’s extrinsic theory, in which a rupture of the amnion explains the anomalies. When placentocranial adhesions occur, causative factors could include a short umbilical cord, an encephalocele, or intrauterine trauma.
Declaration of patient consent
The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.
Financial support and sponsorship
Conflicts of interest
There are no conflicts of interest.
| References|| |
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