Journal of Pediatric Neurosciences
ORIGINAL ARTICLE
Year
: 2012  |  Volume : 7  |  Issue : 3  |  Page : 167--170

Split cord malformation with dorsally located bony spur: Report of four cases and review of literature


GL Prasad, Sachin A Borkar, GD Satyarthee, AK Mahapatra 
 Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi, India

Correspondence Address:
A K Mahapatra
Department of Neurosurgery, Room No 720, 7th Floor, C N Centre, All India Institute of Medical Sciences, Ansari Nagar, New Delhi - 110 029
India

Split cord malformations (SCM) with a dorsally located bony spur are a very rare entity. The authors report a series of four such cases. The literature is reviewed regarding the pathogenesis and management of this uncommon variant of SCM. The presenting features include - scoliosis with motor and autonomic dysfunction (n = 1), scoliosis with cutaneous patch (n = 1), hypertrichotic area (n = 1), and motor deficits alone (n = 1). The location of spur was thoracic and lumbar in two patients (50%) each. Low-lying conus was present in three patients. Long segment syrinx was present in one patient. With respect to the bony anomalies, two patients had a hypertrophied posterior arch (HPA) and one patient had a dysraphic spine. All patients underwent surgical excision of the spur with detethering, if a low-lying conus was present. Two patients developed transient worsening of the neurological status after surgery which recovered at the time of the last follow-up; in both these patients, there was a HPA and a low-lying conus. Surgical excision of the spur with detethering of filum, in cases of low-lying conus, is the treatment of choice. Risk of post-operative worsening of the neurological status is increased in cases in which there is concomitant presence of HPA.


How to cite this article:
Prasad G L, Borkar SA, Satyarthee G D, Mahapatra A K. Split cord malformation with dorsally located bony spur: Report of four cases and review of literature.J Pediatr Neurosci 2012;7:167-170


How to cite this URL:
Prasad G L, Borkar SA, Satyarthee G D, Mahapatra A K. Split cord malformation with dorsally located bony spur: Report of four cases and review of literature. J Pediatr Neurosci [serial online] 2012 [cited 2023 Jan 31 ];7:167-170
Available from: https://www.pediatricneurosciences.com/article.asp?issn=1817-1745;year=2012;volume=7;issue=3;spage=167;epage=170;aulast=Prasad;type=0